Exercise Training as Part of Musculoskeletal Management for Congenital Myopathy: Where Are We Now?

ResearchSpace Repository

Show simple item record

dc.contributor.author Adaikina, Alena en
dc.contributor.author Hofman, Paul en
dc.contributor.author O'Grady, Gina L en
dc.contributor.author Gusso, Silmara en
dc.date.accessioned 2020-02-11T23:28:26Z en
dc.date.issued 2020-03 en
dc.identifier.citation Pediatric Neurology 104, 13-18, 2020 en
dc.identifier.issn 0887-8994 en
dc.identifier.uri http://hdl.handle.net/2292/49934 en
dc.description.abstract Congenital myopathy is a heterogeneous group of muscle disorders characterized by muscle weakness and hypotonia. This condition is associated with a range of skeletal, respiratory, and ophthalmologic complications and requires a multidisciplinary therapeutic approach aimed at maximizing the function and independence of patients. One promising direction for therapeutic intervention is physical exercise rehabilitation, given its demonstrated ability to promote muscle and bone health of patients with a variety of neuromuscular conditions. However, there are few data to assist health care professionals identify the optimal physical activity levels and exercise type, including the intensity, frequency, and duration. This lack of empirical evidence is particularly problematic given the fact that inappropriate exercise modes can potentially cause muscle damage in patients with congenital myopathy. In this article, we discuss the rationale behind the incorporation of two types of physical exercises, strength and aerobic training, into the clinical care of patients with congenital myopathy. Given the paucity of literature on the management of congenital myopathy, we review the results of published research on the treatment of both congenital myopathy and other neuromuscular diseases that could provide helpful insights into the physical rehabilitation of patients with congenital myopathy. We also discuss the potential benefits of vibration therapy, which has been studied in patients with other neuromuscular disorders over the last two decades. We conclude by proposing directions for future research on physical rehabilitation of patients with congenital myopathy. en
dc.format.medium Print-Electronic en
dc.language eng en
dc.relation.ispartofseries Pediatric Neurology en
dc.rights Items in ResearchSpace are protected by copyright, with all rights reserved, unless otherwise indicated. Previously published items are made available in accordance with the copyright policy of the publisher. en
dc.rights.uri https://researchspace.auckland.ac.nz/docs/uoa-docs/rights.htm en
dc.rights.uri https://creativecommons.org/licenses/by-nc-nd/4.0/ en
dc.title Exercise Training as Part of Musculoskeletal Management for Congenital Myopathy: Where Are We Now? en
dc.type Journal Article en
dc.identifier.doi 10.1016/j.pediatrneurol.2019.10.008 en
pubs.begin-page 13 en
pubs.volume 104 en
dc.rights.holder Copyright: The authors en
pubs.end-page 18 en
pubs.publication-status Published en
dc.rights.accessrights http://purl.org/eprint/accessRights/OpenAccess en
pubs.subtype Research Support, Non-U.S. Gov't en
pubs.subtype Review en
pubs.subtype Journal Article en
pubs.elements-id 792752 en
pubs.org-id Liggins Institute en
pubs.org-id Medical and Health Sciences en
pubs.org-id Nursing en
pubs.org-id Science en
pubs.org-id Exercise Sciences en
dc.identifier.eissn 1873-5150 en
pubs.record-created-at-source-date 2020-01-14 en
pubs.dimensions-id 31926608 en

Files in this item

Find Full text

This item appears in the following Collection(s)

Show simple item record

https://creativecommons.org/licenses/by-nc-nd/4.0/ Except where otherwise noted, this item's license is described as https://creativecommons.org/licenses/by-nc-nd/4.0/


Search ResearchSpace

Advanced Search